Felty syndrome

Description

Felty's syndrome: Felty syndrome (FS), also known as ''super rheumatoid'' disease, is a severe form of rheumatoid arthritis (RA), characterized by a triad of RA, splenomegaly and neutropenia, resulting in susceptibility to bacterial infections.

Data source
FinnGen phenocode FELTY
Hospital Discharge registry ICD-10: M050, ICD-8: 71210
Cause of Death registry ICD-10: M050, ICD-8: 71210
First defined in version DF2
Ontology
DOID 11042
GWAS catalog 0007269
MESH D005258
SNOMED CT 57160007

Key figures

Sex All Female Male
Number of individuals 36 24 12
Unadjusted prevalence (%) 0.03 0.03 0.02
Mean age at first event (years) 63.86 65.07 61.44
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 25.0 25.0 25.0
Case fatality at 5-years (%) 13.89 20.83 0.0

Associations