Other and unspecified bullous disorders

Description

subcorneal pustular dermatosis: a rare, benign, chronic relapsing sterile pustular eruption typically involving the flexural sites of the trunk and proximal extremities. It most commonly affects woman aged 40 years or older.

Data source
FinnGen phenocode L12_OTHERBULL
Hospital Discharge registry ICD-10: L13, ICD-8: 69409
Hospital Discharge registry: exclude ICD-10 L13[0-1]
Cause of Death registry ICD-10: L13, ICD-8: 69409|69402
Cause of Death registry: exclude ICD-10 L13[0-1]
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 8508
GWAS catalog 1000771
SNOMED CT 25147002

Key figures

Sex All Female Male
Number of individuals 60 33 27
Unadjusted prevalence (%) 0.05 0.04 0.05
Mean age at first event (years) 57.35 57.74 56.87
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 15.0 12.12 18.52
Case fatality at 5-years (%) 10.0 9.09 11.11

Associations