Behçet disease
Description
Behcet's syndrome: Bechet disease (BD) is a chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations.
Data source
| FinnGen phenocode | M13_BEHCET |
| Hospital Discharge registry | ICD-10: M352 |
| Cause of Death registry | ICD-10: M352 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 20 | 14 | 6 |
| Unadjusted prevalence (%) | 0.02 | 0.02 | 0.01 |
| Mean age at first event (years) | 48.21 | 44.79 | 56.18 |
| Median number of events / individual | 3 | 4 | 1 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 55.0 | 64.29 | 33.33 |
| Case fatality at 5-years (%) | 5.0 | 7.14 | 0.0 |