Other and unspecified malignant neoplasms of lymphoid, haematopoietic and related tissue

Description

Mast Cell Sarcoma: A rare entity characterized by localized but destructive growth of a tumor consisting of highly atypical, immature mast cells.(WHO, 2001)

Data source
FinnGen phenocode CD2_PRIMARY_LYMPHOID_HEMATOPOIETIC_NAS
Hospital Discharge registry ICD-10: C96
Cause of Death registry ICD-10: C96
Level in the ICD-hierarchy 3
First defined in version DF2
Ontology
DOID 355
GWAS catalog 1000364
MESH D012515
SNOMED CT 118615008

Key figures

Sex All Female Male
Number of individuals 36 20 16
Unadjusted prevalence (%) 0.03 0.03 0.03
Mean age at first event (years) 61.87 62.96 60.5
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 22.22 25.0 18.75
Case fatality at 5-years (%) 11.11 15.0 6.25

Associations