Biliary chirrosis, NAS
Description
primary biliary cirrhosis: Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.
Data source
| FinnGen phenocode | CHIRBIL_NAS |
| Hospital Discharge registry | ICD-10: K745 |
| Cause of Death registry | ICD-10: K745 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 25 | 19 | 6 |
| Unadjusted prevalence (%) | 0.02 | 0.03 | 0.01 |
| Mean age at first event (years) | 65.06 | 63.58 | 69.74 |
| Median number of events / individual | 1 | 1 | 1 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 40.0 | 42.11 | 33.33 |
| Case fatality at 5-years (%) | 12.0 | 5.26 | 33.33 |