Biliary chirrosis, primary
Description
primary biliary cirrhosis: Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.
Data source
| FinnGen phenocode | CHIRBIL_PRIM |
| Hospital Discharge registry | ICD-10: K743 |
| Cause of Death registry | ICD-10: K743 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 143 | 125 | 18 |
| Unadjusted prevalence (%) | 0.11 | 0.17 | 0.03 |
| Mean age at first event (years) | 57.64 | 57.29 | 60.05 |
| Median number of events / individual | 7 | 7 | 6 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 76.92 | 76.0 | 83.33 |
| Case fatality at 5-years (%) | 4.9 | 4.8 | 5.56 |