Immunodeficiency associated with other major defects

Description

No definition available.

Data source
FinnGen phenocode D3_IMMUDEFWITHMAJORDEF
Hospital Discharge registry ICD-10: D82
Cause of Death registry ICD-10: D82
Include D3_WISKOTTALDRICH, D3_DIGEORGE, D3_IMMUDEFSHORTLIMB, D3_IMMUDEFPOSTEBV, D3_HYPERIGESDR, D3_IMMUDEFMAJORDEFNAS
Level in the ICD-hierarchy 3
First defined in version DF2

Key figures

Sex All Female Male
Number of individuals 19 10 9
Unadjusted prevalence (%) 0.01 0.01 0.02
Mean age at first event (years) 55.0 58.63 50.96
Median number of events / individual 1 1 2

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 47.37 40.0 55.56
Case fatality at 5-years (%) 10.53 10.0 11.11

Associations