Severe combined immunodeficiency [SCID] with reticular dysgenesis
Description
No definition available.
Data source
| FinnGen phenocode | D3_SCIDA |
| Hospital Discharge registry | ICD-10: D810 |
| Cause of Death registry | ICD-10: D810 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 25 | 11 | 14 |
| Unadjusted prevalence (%) | 0.02 | 0.01 | 0.02 |
| Mean age at first event (years) | 54.19 | 45.4 | 61.09 |
| Median number of events / individual | 1 | 1 | 1 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 4.0 | 9.09 | N/A |
| Case fatality at 5-years (%) | 0.0 | 0.0 | 0.0 |