Localized scleroderma [morphea]

Description

localised scleroderma: Localized scleroderma is the skin localized form of scleroderma (see this term) characterized by fibrosis of the skin causing cutaneous plaques or strips.

Data source
FinnGen phenocode L12_LOCALSCLERODERMA
Hospital Discharge registry ICD-10: L940, ICD-9: 7010A, ICD-8: 70100
Cause of Death registry ICD-10: L940, ICD-9: 7010A, ICD-8: 70100
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 419, 8472
GWAS catalog 1001361
MESH D012594
SNOMED CT 201048007

Key figures

Sex All Female Male
Number of individuals 99 80 19
Unadjusted prevalence (%) 0.07 0.11 0.03
Mean age at first event (years) 49.65 50.12 47.68
Median number of events / individual 2 2 2

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 50.51 51.25 47.37
Case fatality at 5-years (%) 1.01 1.25 0.0

Associations