Cicatricial pemphigoid

Description

mucous membrane pemphigoid: Mucous membrane pemphigoid is a bullous dermatosis characterised clinically by blistering of the mucous membranes followed by scarring, and immunologically by IgG, IgA and/or C3 deposits on the epidermal basement membrane.

Data source
FinnGen phenocode L12_PEMPHIGOID_CICA
Hospital Discharge registry ICD-10: L121
Cause of Death registry ICD-10: L121
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 11656
GWAS catalog 1000680
SNOMED CT 76092003

Key figures

Sex All Female Male
Number of individuals 15 11 N/A
Unadjusted prevalence (%) 0.01 0.01 N/A
Mean age at first event (years) 63.78 60.42 N/A
Median number of events / individual 3 3 N/A

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 60.0 54.55 N/A
Case fatality at 5-years (%) 0.0 0.0 N/A

Associations