Other and unspecified pemphigus

Description

pemphigus: a rare group of blistering autoimmune diseases that affect the skin and mucous membranes.

Data source
FinnGen phenocode L12_PEMPHIGUS_NAS
Hospital Discharge registry ICD-10: L109/L108, ICD-8: 69400|69403
Cause of Death registry ICD-10: L108/L109, ICD-8: 69400|69403
KELA reimboursements codes ANY
KELA reimbursements ICD-10: L10
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 9182
GWAS catalog 1000749
MESH D010392
SNOMED CT 65172003

Key figures

Sex All Female Male
Number of individuals 20 11 9
Unadjusted prevalence (%) 0.02 0.01 0.02
Mean age at first event (years) 55.23 50.99 60.41
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 30.0 36.36 22.22
Case fatality at 5-years (%) 10.0 0.0 22.22

Associations