Pemphigus vulgaris

Description

pemphigus vulgaris: Pemphigus vulgaris is a rare chronic blistering skin disease and the most common form of pemphigus.

Data source
FinnGen phenocode L12_PEMPHIGUS_VULG
Hospital Discharge registry ICD-10: L100, ICD-9: 6944A
Cause of Death registry ICD-10: L100, ICD-9: 6944A
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 0060851
GWAS catalog 0004719
SNOMED CT 49420001

Key figures

Sex All Female Male
Number of individuals 13 7 6
Unadjusted prevalence (%) 0.01 0.01 0.01
Mean age at first event (years) 49.86 44.81 55.75
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 23.08 28.57 16.67
Case fatality at 5-years (%) 0.0 0.0 0.0

Associations