Ankylosing hyperostosis [Forestier]
Description
diffuse idiopathic skeletal hyperostosis: This syndrome is characterized by the association of ankylosing vertebral hyperostosis with hyperkeratosis of the soles and palms.
Data source
FinnGen phenocode | M13_FORESTIER |
Hospital Discharge registry | ICD-10: M481 |
Cause of Death registry | ICD-10: M481 |
Level in the ICD-hierarchy | 4 |
First defined in version | DF2 |
Key figures
Sex | All | Female | Male |
Number of individuals | 103 | 45 | 58 |
Unadjusted prevalence (%) | 0.08 | 0.06 | 0.1 |
Mean age at first event (years) | 56.11 | 55.93 | 56.25 |
Median number of events / individual | 1 | 1 | 1 |
Clinical metrics
Sex | All | Female | Male |
Recurrence within 6 months (%) | 22.33 | 26.67 | 18.97 |
Case fatality at 5-years (%) | 3.88 | 2.22 | 5.17 |