Ganglion

Description

ganglioneuroblastoma: A neuroblastic tumor characterized by the presence of neuroblastic cells, ganglion cells, and a stroma with Schwannian differentiation constituting more than fifty-percent of the tumor volume. There are two histologic subtypes identified: ganglioneuroblastoma, intermixed and ganglioneuroblastoma, nodular.

Data source
FinnGen phenocode M13_GANGLION
Hospital Discharge registry ICD-10: M674
Cause of Death registry ICD-10: M674
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 4163
GWAS catalog 0000502
SNOMED CT 116381000119105

Key figures

Sex All Female Male
Number of individuals 2272 1619 653
Unadjusted prevalence (%) 1.71 2.15 1.14
Mean age at first event (years) 46.07 45.22 48.18
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 24.25 25.08 22.21
Case fatality at 5-years (%) 0.62 0.25 1.53

Associations