Mucocutaneous lymph node syndrome [Kawasaki]

Description

mucocutaneous lymph node syndrome: Kawasaki disease (KD) is a febrile, systemic, self-limiting vasculitis affecting children and characterized by inflammation in the medium sized vessels associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. KD is the most common cause of acquired heart disease in children in developed countries and is a risk factor for ischemic heart disease in adulthood.

Data source
FinnGen phenocode M13_KAWASAKI
Hospital Discharge registry ICD-10: M303
Cause of Death registry ICD-10: M303
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 13378
GWAS catalog 0004246
MESH D009080
SNOMED CT 75053002

Key figures

Sex All Female Male
Number of individuals 7 6 N/A
Unadjusted prevalence (%) 0.01 0.01 N/A
Mean age at first event (years) 37.09 41.65 N/A
Median number of events / individual 2 2 N/A

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 28.57 33.33 N/A
Case fatality at 5-years (%) 0.0 0.0 N/A

Associations