Relapsing polychondritis
Description
relapsing polychondritis: Relapsing polychondritis (RP) is a rare, clinically heterogeneous, multisystemic inflammatory disease characterized by inflammation of the cartilage and proteoglycan rich structures leading to cartilage damage with joint, ocular and cardiovascular involvement.
Data source
| FinnGen phenocode | M13_RELAPSPOLYCHONDR |
| Hospital Discharge registry | ICD-10: M941 |
| Cause of Death registry | ICD-10: M941 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 14 | 7 | 7 |
| Unadjusted prevalence (%) | 0.01 | 0.01 | 0.01 |
| Mean age at first event (years) | 52.69 | 50.2 | 55.18 |
| Median number of events / individual | 7 | 9 | 6 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 71.43 | 71.43 | 71.43 |
| Case fatality at 5-years (%) | 0.0 | 0.0 | 0.0 |