Aortic arch syndrome [Takayasu]
Description
Takayasu arteritis: Takayasu arteritis (TAK) is a rare inflammatory large-vessel vasculitis primarily affecting the aorta and its major branches, but also other large vessels, causing stenosis, occlusion, or aneurysm.
Data source
| FinnGen phenocode | M13_TAKAYASU |
| Hospital Discharge registry | ICD-10: M314 |
| Cause of Death registry | ICD-10: M314 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 14 | 10 | N/A |
| Unadjusted prevalence (%) | 0.01 | 0.01 | N/A |
| Mean age at first event (years) | 50.18 | 47.26 | N/A |
| Median number of events / individual | 8 | 4 | N/A |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 64.29 | 60.0 | N/A |
| Case fatality at 5-years (%) | 0.0 | 0.0 | N/A |