Wegener granulomatosis
Description
Granulomatosis with Polyangiitis: A small-vessel necrotizing vasculitis characterised by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis.
Data source
| FinnGen phenocode | M13_WEGENER |
| Hospital Discharge registry | ICD-10: M313, ICD-8: 4462 |
| Cause of Death registry | ICD-10: M313, ICD-8: 4462 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 121 | 63 | 58 |
| Unadjusted prevalence (%) | 0.09 | 0.08 | 0.1 |
| Mean age at first event (years) | 53.75 | 52.53 | 55.08 |
| Median number of events / individual | 8 | 3 | 20 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 71.07 | 63.49 | 79.31 |
| Case fatality at 5-years (%) | 4.96 | 4.76 | 5.17 |