Other systemic involvement of connective tissue

Description

nodular nonsuppurative panniculitis: a rare group of skin disorders characterized by tender, painful bumps below the surface of the skin (subcutaneous nodules) that usually lead to inflammation of the subcutaneous layer of fat (panniculitis). These nodules tend to be 1-2 centimeters in length and most often affect the legs and feet.

Data source
FinnGen phenocode M13_OTHCONN
Hospital Discharge registry ICD-10: M35
Cause of Death registry ICD-10: M35
Include M13_SJOGREN, M13_OVERLAP, M13_BEHCET, M13_POLYMYALGIA, M13_DIFFASCITIS, M13_MULTIFIBRO, M13_WEBERCHRISTIAN, M13_HYPERMOBILITY, M13_CONNECTNAS, M13_SYSTCONINOTH
Level in the ICD-hierarchy 3
First defined in version DF2
Ontology
DOID 1525
GWAS catalog 1000742
MESH D010201
SNOMED CT 33760009

Key figures

Sex All Female Male
Number of individuals 2366 1845 521
Unadjusted prevalence (%) 1.78 2.46 0.91
Mean age at first event (years) 55.96 54.75 60.26
Median number of events / individual 2 2 2

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 50.8 51.87 47.02
Case fatality at 5-years (%) 5.03 3.85 9.21

Associations