Adult-onset Still disease
Description
adult-onset Still's disease: adult-onset Still disease (AOSD) is a rare inflammatory multisystem disorder characterized clinically by fever of unknown origin, arthralgia or arthritis, hyperleucocytosis, and typical skin rash.
Data source
| FinnGen phenocode | STILL_ADULT |
| Hospital Discharge registry | ICD-10: M060 |
| Cause of Death registry | ICD-10: M060 |
| Include | STILL_ADULT, RHEUMA_NOS, RHEUMA_OTHER_WIDE |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 1988 | 1418 | 570 |
| Unadjusted prevalence (%) | 1.5 | 1.89 | 0.99 |
| Mean age at first event (years) | 49.98 | 49.22 | 51.88 |
| Median number of events / individual | 3 | 3 | 3 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 54.23 | 55.43 | 51.23 |
| Case fatality at 5-years (%) | 3.12 | 2.4 | 4.91 |