Combined immunodeficiencies
Description
No definition available.
Data source
FinnGen phenocode | D3_COMBIMMUDEF |
Hospital Discharge registry | ICD-10: D81 |
Cause of Death registry | ICD-10: D81 |
Include | D3_SCIDA, D3_SCIDB, D3_SCIDC, D3_ADA_DEF, D3_NEFELOF, D3_PNP_DEF, D3_COMPXI, D3_COMPXII, D3_OCID, D3_COMBIMMUDEFNAS |
Level in the ICD-hierarchy | 3 |
First defined in version | DF2 |
Key figures
Sex | All | Female | Male |
Number of individuals | 97 | 64 | 33 |
Unadjusted prevalence (%) | 0.07 | 0.09 | 0.06 |
Mean age at first event (years) | 55.56 | 52.41 | 61.68 |
Median number of events / individual | 1 | 1 | 1 |
Clinical metrics
Sex | All | Female | Male |
Recurrence within 6 months (%) | 6.19 | 6.25 | 6.06 |
Case fatality at 5-years (%) | 6.19 | 7.81 | 3.03 |