Combined immunodeficiencies

Description

No definition available.

Data source
FinnGen phenocode D3_COMBIMMUDEF
Hospital Discharge registry ICD-10: D81
Cause of Death registry ICD-10: D81
Include D3_SCIDA, D3_SCIDB, D3_SCIDC, D3_ADA_DEF, D3_NEFELOF, D3_PNP_DEF, D3_COMPXI, D3_COMPXII, D3_OCID, D3_COMBIMMUDEFNAS
Level in the ICD-hierarchy 3
First defined in version DF2

Key figures

Sex All Female Male
Number of individuals 97 64 33
Unadjusted prevalence (%) 0.07 0.09 0.06
Mean age at first event (years) 55.56 52.41 61.68
Median number of events / individual 1 1 1

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 6.19 6.25 6.06
Case fatality at 5-years (%) 6.19 7.81 3.03

Associations