Bullous disorders
Description
subcorneal pustular dermatosis: a rare, benign, chronic relapsing sterile pustular eruption typically involving the flexural sites of the trunk and proximal extremities. It most commonly affects woman aged 40 years or older.
Data source
FinnGen phenocode | L12_BULLOUS |
Include | L12_PEMPHIGUS, L12_ACANTHOLYTIC, L12_PEMPHIGOID, L12_BULLOTH, L12_BULLOUSINOTH, L12_PEMPHIKELA |
Level in the ICD-hierarchy | 2 |
First defined in version | DF2 |
Key figures
Sex | All | Female | Male |
Number of individuals | 428 | 249 | 179 |
Unadjusted prevalence (%) | 0.32 | 0.33 | 0.31 |
Mean age at first event (years) | 55.76 | 54.47 | 57.55 |
Median number of events / individual | 2 | 2 | 2 |
Clinical metrics
Sex | All | Female | Male |
Recurrence within 6 months (%) | 48.13 | 44.58 | 53.07 |
Case fatality at 5-years (%) | 10.51 | 9.24 | 12.29 |