Pemphigoid

Description

juvenile dermatitis herpetiformis: dermatitis herpetiformis in children

Data source
FinnGen phenocode L12_PEMPHIGOID
Hospital Discharge registry ICD-10: L12
Cause of Death registry ICD-10: L12
Include L12_PEMPHIGOID_BULL, L12_PEMPHIGOID_CICA, L12_BULLLOUS_CHILD, L12_EPIDERMOLYSIS_ACQ, L12_PEMPHIGOID_NAS
Level in the ICD-hierarchy 3
First defined in version DF2
Ontology
DOID 8507
GWAS catalog 1000719
SNOMED CT 5906000

Key figures

Sex All Female Male
Number of individuals 167 95 72
Unadjusted prevalence (%) 0.13 0.13 0.13
Mean age at first event (years) 66.99 66.61 67.5
Median number of events / individual 3 3 3

Clinical metrics

Sex All Female Male
Recurrence within 6 months (%) 67.66 66.32 69.44
Case fatality at 5-years (%) 19.76 20.0 19.44

Associations