Other localized connective tissue disorders
Description
localised scleroderma: Localized scleroderma is the skin localized form of scleroderma (see this term) characterized by fibrosis of the skin causing cutaneous plaques or strips.
Data source
| FinnGen phenocode | L12_LOCALDCONNECTISSUEOTH |
| Hospital Discharge registry | ICD-10: L94 |
| Cause of Death registry | ICD-10: L94 |
| Include | L12_LOCALSCLERODERMA, L12_LINEARSCLERODERMA, L12_CALCINOSISCUTIS, L12_SCLERODACTYLY, L12_GOTTRONPAPULES, L12_POIKILODERMAVASCULAREATROPH, L12_AINHUM, L12_LOCALCONNECTISSUENAS |
| Level in the ICD-hierarchy | 3 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 134 | 104 | 30 |
| Unadjusted prevalence (%) | 0.1 | 0.14 | 0.05 |
| Mean age at first event (years) | 50.05 | 50.37 | 48.92 |
| Median number of events / individual | 2 | 2 | 2 |
Clinical metrics
| Sex | All | Female | Male |
| Recurrence within 6 months (%) | 48.51 | 47.12 | 53.33 |
| Case fatality at 5-years (%) | 3.73 | 3.85 | 3.33 |